Meaning of the word "Tay-Sachs Disease" in English

What does "Tay-Sachs Disease" mean in English? Explore the meaning, pronunciation, and specific usage of this word with Lingoland.

Tay-Sachs Disease

US /ˌteɪ ˈsæks dɪˌziːz/
UK /ˌteɪ ˈsæks dɪˌziːz/
"Tay-Sachs Disease" picture

Noun

a rare, inherited disorder that progressively destroys nerve cells in the brain and spinal cord. It is caused by the absence of a vital enzyme called beta-hexosaminidase A, which leads to the buildup of a fatty substance (GM2 ganglioside) in cells, particularly in the brain.

Example:
Children with Tay-Sachs Disease often show symptoms like developmental delay and a cherry-red spot in the eye.
Genetic counseling is important for families with a history of Tay-Sachs Disease.